7 Nov Me llamo Loli tengo 37 años y vivo en Madrid y me diagnoticaron la enfermedad de Degos en despues de que perdiera la vision del ojo. Se describe el caso de una mujer de 60 años de edad que presentaba desde hacía años lesiones hiperpigmentadas reticuladas que afectaban a los pliegues . Enfermedad de Dowling-Degos: caso clínico asociado a hidradenitis supurativa. Dowling-Degos Disease Associated With Hidradenitis Suppurativa: A Case.
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Later a wedge-shaped connective tissue necrosis in the deep dermis, due to a thrombotic occlusion of the small arteries and sparse lymphocytes, occurs. Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of enfrmedad lesions in some individual cases.
MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on degs trunk and the upper extremities.
This page was last edited on 25 Septemberat This correspondence has been reviewed by an OTRS member and stored in our permission archive. More developed lesions can imitate lichen sclerosus see this term. Management and treatment Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
Health care resources for this disease Expert centres 65 Diagnostic tests 0 Patient organisations 19 Orphan drug s 0. Hypotheses implicating vasculitis, coagulopathy or a primary dysfunction of endothelial cells have been proposed. More devos lesions show prominent changes in the dermoepidermal junction, with atrophy of the epidermis and an area of sclerosis in the papillary dermis.
Enfermedad de Degos
Systemic manifestations are progressive and may lead to serious complications: This work enfermedaf free and may be used by anyone for any purpose. A clinical inspection of the skin should be combined with additional examinations including brain magnetic resonance tomography, gastroscopy, colonoscopy, X-ray of the chest and abdominal ultrasound, in order to assess the long-term prognosis. Summary and related texts. Degos disease Injured human backs.
Over several days, the center of the lesions sinks and develops a characteristic morphology: The histology of early lesions resembles cutaneous lupus erythematosus see this term. Many patients have been reported to have defects in blood coagulation. Prognosis Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions.
Retrieved from ” https: Differential diagnosis The histology of early lesions resembles cutaneous lupus erythematosus see this term. In early stages, histology of lesions may reveal a superficial and deep perivascular lymphocytic infiltration with distinct mucin deposition.
Enfermedad de Dowling-Degos – ScienceDirect
The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment. The following other wikis use this file: Diagnostic methods Diagnosis is based primarily enfermedac the endermedad clinical picture that is nearly pathognomonic. Thomas Habif authorises the use enfermedxd the 21 pictures listed here and published on the website dermnet.
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Etiology The etiopathogenesis of the disease remains unknown. Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Summary [ edit ] Description Degos-disease.
Ocular involvement, which affects the eyelids, conjuctiva, retina, sclera and the nefermedad plexus, as well as the development of diplopia and ophthalmoplegia as secondary side effects of the neurologic involvementhas also been described. Views View Edit History.
Disease definition Malignant atrophic papulosis MAP is a rare, enfefmedad, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim.